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Case Report

An unusual reason for complete atrioventricular block ; Kearn Sayre Syndrome

Halil Atas, Fuad Samadov, Osman Yesildag

   

Abstract
Kearn sayre syndrome (KSS) is a rare disease with a typical onset before 20 years and charactarized by triad of chronic progressive external ophthalmoplegia, retinitis pigmentosa and progressive cardiac conduction abnormalities. The most important prognostic factor in KSS patients is the involvement of heart characterized by progressive degeneration of the conduction system. In patients with KSS, early diagnosis of cardiac involvement is very important because complete atrioventricular (AV) block may develop and it can be cause of sudden cardiac death. Herein we report a patients with KSS who presented with syncope due to complete AV block .

Key words: Kearn sayre syndrome, atrioventricular block, disease

Med-Science. 2016; 5(4): 1005-7

Medicine Science Vol:5 Issue:4 Year:2016 PP:919-1084
Posted in Vol: 5 Issue: 4 Year: 2016 December pp: 919-1084

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